SEER Inquiry System - View
Source 1: ICD-O-3
Reportability--Brain and CNS: Is this case reportable? See discussion.
The pathologic diagnosis is:
Cranium, right temporal area, resection of intradural, extra-axial mass: severe acute and chronic inflammation, histiocytic reaction, and proliferative fibrosis. See comment.
Comment: Among potential alternative considerations are an infectious process, or non-infectious inflammatory CNS lesions such as inflammatory pseudotumor, Rosai-Dorfman disease, plasma cell granuloma, ideopathic hypertrophic pachymeningitis, and inflammatory myofibroblastic tumor.
The clinicians discuss this and review other chart information and conclude with a clinical diagnosis of Rosai-Dorfman disease.
This is a rare disorder characterized by proliferation of histiocytes. This is clearly benign, but is it considered neoplastic, and is it reportable if it occurs in the brain?
This case is not reportable. Rosai-Dorfman disease is not listed in ICD-O-3. A neoplasm must be listed in ICD-O-3 and originate in a reportable site to be reportable for brain/CNS.